Focal nodulary hyperplasia of the liver due to congenital portosystemic shunt: A rare condition mimicking hepatocellulary carcinoma

Erdem A. Y. , Emir S., Demir H. A. , Ozyoruk D., Cetin İ. İ. , Turan A., ...More

Journal of Pediatric Hematology/Oncology, vol.39, no.1, 2017 (Peer-Reviewed Journal) identifier identifier

  • Publication Type: Article / Article
  • Volume: 39 Issue: 1
  • Publication Date: 2017
  • Doi Number: 10.1097/mph.0000000000000666
  • Journal Name: Journal of Pediatric Hematology/Oncology
  • Journal Indexes: Science Citation Index Expanded, Scopus
  • Keywords: Congenital portosystemic shunt, Focal nodulary hyperplasia


Copyright © 2016 Wolters Kluwer Health, Inc. All rights reserved.Congenital portosystemic shunts are rare vascular malformations that lead to several complications including liver tumors, pulmonary hypertension, and metabolic encephalopathy. We describe a rare case of a 17-year-old girl with an extrahepatic portosystemic shunt presenting recurrent syncope episodes and a liver mass mimicking hepatocellulary carcinoma.