Comparison of surgical outcomes of total colonic aganglionosis with the short and long – Hirschsprung disease

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Öztorun C. İ., Erten E. E., Bostancı S. A., Ertürk A., Çayhan V. S., Uzun A. U., ...More

7th World Congress of the World Federation of Associations of Pediatric Surgeons (WOFAPS), Praha, Czech Republic, 12 - 15 October 2022, pp.67-68, (Summary Text)

  • Publication Type: Conference Paper / Summary Text
  • City: Praha
  • Country: Czech Republic
  • Page Numbers: pp.67-68
  • Ankara Yıldırım Beyazıt University Affiliated: Yes

Abstract

Aim: Total colonic aganglionosis (TCA) is a rare form of Hirschsprung disease (HD), with more severe symptoms

than rectosigmoid Hirschsprung disease. We aimed to compare the surgical outcomes of TCA with

Short- HD, and Long-HD.

Methods: We evaluated the patients with HD and compared the patients according to the location of the

aganglionic segment in terms of demographic data, surgery, length of hospital stay, and short and long-term

complication. The medical records of 102 patients with HD from 2000 to 2021 were reviewed

Results: The patients included in this study were divided into three groups TCA(n=15), Short- HD (n=82), and

Long-HD (n=5) according to the involved aganglionic segment. The data about the patients and surgical outcomes

of the groups are shown in table 1. In our series, % 14,7 HD patients were TCA. The mean age at the

definitive surgery was 18.2 (1–152) months. The most common methods of definitive surgery was TEPT and

Duhamel procedure. Perianal excoriation and enterocolitis were the most common postoperative complications.

The complication and mortality rates were higher in Long-HD and TCA groups.

Conclusion: In the study, it was found that symptoms were seen earlier, diagnosis and definitive surgery

were performed earlier in patients in TCA group compared to other groups. The length of hospital stay was

longer in the TCA group. Except for the higher incidence of perianal excoriation in the TCA group, there were

no significant differences between the groups in terms of the incidence of postoperative complications, especially

enterocolitis. However, the mortality rate is higher in TCA and Long-HD group