Pulmonary embolism in a patient with Klippel-Trenaunay-Weber syndrome

KARALEZLİ A., Sevgili S., Ernam Turgut D., Hasanoǧlu A., HASANOĞLU H. C.

Tuberkuloz ve Toraks, vol.54, no.3, pp.281-287, 2006 (Scopus) identifier identifier

  • Publication Type: Article / Article
  • Volume: 54 Issue: 3
  • Publication Date: 2006
  • Journal Name: Tuberkuloz ve Toraks
  • Journal Indexes: Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.281-287
  • Keywords: Deep venous thrombosis, Klippel-Trenaunay-Weber syndrome, Pulmonary embolism
  • Ankara Yıldırım Beyazıt University Affiliated: Yes

Abstract

Klippel-Trenaunay-Weber syndrome (KTWS) is a congenital disorder characterized by cutaneous capillary malformations, venous-lymphatic anomalies, hypertrophy of soft tissue and bone in the area of increased vascularity and arteriouenous fistulas with shunting. In this article we report the case of a 25 years old man with KTWS who had multiple surgical operations because of arteriovenous malformations. He admitted with pulmonary embolism attack to the hospital although he was taking prophylactic heparin treatment. We evaluate the risk of pulmonary embolism in patients with KTWS, being aware of the risk of deep venous thrombosis in progress of the disease and the importance of early diagnosis in prognosis.