Severe peripheral pulmonary artery stenosis is not a contraindication to liver transplantation in Alagille syndrome
Pediatric Transplantation, cilt.10, sa.1, ss.108-111, 2006 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 10 Sayı: 1
- Basım Tarihi: 2006
- Doi Numarası: 10.1111/j.1399-3046.2005.00390.x
- Dergi Adı: Pediatric Transplantation
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.108-111
- Anahtar Kelimeler: Alagille syndrome, Liver transplantation, Pulmonary stenosis
- Ankara Yıldırım Beyazıt Üniversitesi Adresli: Hayır
Özet
We described a case of Alagille syndrome with severe peripheral pulmonary artery stenosis and very high right ventricular pressure that underwent successful living-related liver transplantation without any peri-operative and mid-term postoperative complication because of this cardiac malformation. The aim of this report is to point out that the severe pulmonary artery stenosis may be a risk factor but not a contraindication to liver transplantation in patients with Alagille syndrome. © 2005 Blackwell Munksgaard.